tratamiento nutricional

Bernstein LE, Burns C, Drumm M, Gaughan S, Sailer M, Baker PR 2nd. 

Impact on Isoleucine and Valine Supplementation When Decreasing Use of Medical Food in the Nutritional Management of Methylmalonic Acidemia.  
Nutrients. 2020;12(2):473

pdf

Manoli I, Myles JG, Sloan JL, Shchelochkov OA, Venditti CP. 

A critical reappraisal of dietary practices in methylmalonic acidemia raises concerns about the safety of medical foods. Part 1: isolated methylmalonic acidemias. 

Genet Med. 2016;18(4):386-395. 

pdf

Manoli I, Myles JG, Sloan JL, et al. 

A critical reappraisal of dietary practices in methylmalonic acidemia raises concerns about the safety of medical foods. Part 2: cobalamin C deficiency. 

Genet Med. 2016;18(4):396-404

pdf

Myles JG, Manoli I, Venditti CP. 

Effects of medical food leucine content in the management of methylmalonic and propionic acidemias. Curr Opin Clin Nutr Metab Care. 2018;21(1):42-48 

pdf
Share by: